Williams-Campbell syndrome

Thomas Hartman

Research output: Chapter in Book/Report/Conference proceedingChapter


Imaging Williams-Campbell syndrome is characterized by cystic bronchiectasis in the fourth to sixth order bronchi [1, 2] (Figure 8.1–8.3). If expiratory images are obtained, collapse of the bronchiectatic segments can be seen [1–3]. Hyperinflation or emphysematous changes may also be seen in the lung distal to the bronchiectatic regions. The cause of the bronchiectasis is due to defective or absent cartilage in the walls of the fourth to sixth order bronchi. Importance Williams-Campbell syndrome has been postulated to be a congenital abnormality. At least two separate reports have shown a familial occurrence [3]. Therefore, recognition of this abnormality in a patient should lead to additional investigations of family members.

Original languageEnglish (US)
Title of host publicationPearls and Pitfalls in Thoracic Imaging
Subtitle of host publicationVariants and Other Difficult Diagnoses
PublisherCambridge University Press
Number of pages2
ISBN (Electronic)9780511977701
ISBN (Print)9780521119078
StatePublished - Jan 1 2011

ASJC Scopus subject areas

  • Medicine(all)


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