Abstract
Pulmonary vasculitis is usually but one manifestation of a systemic autoimmune disease. Primary vasculitis syndromes commonly affecting the respiratory tract are Wegener’s granulomatosis (WG), microscopic polyangiitis (MPA), and the Churg-Strauss syndrome. They are small-vessel vasculitides characterized by the presence of antineutrophil cytoplasmic autoantibodies (ANCA). This chapter provides an overview for a diagnostic approach to these patients that enables disease severity-adapted therapy. The respiratory manifestations of other vasculitides including Takayasu’s arteritis, Behcet’s disease, and Goodpasture’s disease are also discussed.
Original language | English (US) |
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Title of host publication | Diffuse Lung Disease |
Subtitle of host publication | A Practical Approach, Second Edition |
Publisher | Springer New York |
Pages | 365-386 |
Number of pages | 22 |
ISBN (Electronic) | 9781441997715 |
ISBN (Print) | 9781441997708 |
DOIs | |
State | Published - Jan 1 2012 |
Keywords
- Antineutrophil cytoplasmic autoantibodies
- Churg-strauss syndrome
- Microscopic polyangiitis
- Pulmonary vasculitis
- Wegener’S granulomatosis
ASJC Scopus subject areas
- Medicine(all)