Pneumocytic adenomyoepithelioma: A case providing support for the benignity of this extremely rare pulmonary neoplasm

Brandon T. Nokes, Anjuli M. Brighton, Brandon Larsen, Prasad M. Panse, Staci E. Beamer, Rodrigo Cartin-Ceba, Karen L. Swanson

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Pneumocytic adenomyoepithelioma is an extremely rare and poorly understood pulmonary neoplasm, so experience with this tumor is limited. Since the initial case series where the lesion was first proposed as a distinctive entity, only one additional report has been described. We present a case of pneumocytic adenomyoepithelioma with clinical and radiologic data that provide the first long-term evidence of the benignity of this extremely rare pulmonary neoplasm. We also review the available literature surrounding pneumocytic adenomyoepitheliomas. Our case provides important new data on the behavior of this lesion, as imaging studies showed essentially stable or very slowly progressive disease over the course of approximately 9 years. Collectively, this rare and poorly described lesion appears to behave in an indolent or benign fashion, a notion that our case further supports.

Original languageEnglish (US)
Pages (from-to)40-43
Number of pages4
JournalRespiratory Medicine Case Reports
StatePublished - Jan 1 2018



  • Benign pathology
  • Pneumocytic adenomyoepithelioma
  • Pulmonary neoplasm

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine

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