Peripheral primitive neuroectodermal tumor presenting with diffuse cutaneous involvement and 7;22 translocation

L. M. Smith; R. H. Adams; A. R. Brothman; S. L. Vanderhooft; C. M. Coffin; G. J. D'Angio

doi:10.1002/(SICI)1096-911X(199806)30:6<357::AID-MPO10>3.0.CO;2-F

Peripheral primitive neuroectodermal tumor presenting with diffuse cutaneous involvement and 7;22 translocation

L. M. Smith, R. H. Adams, A. R. Brothman, S. L. Vanderhooft, C. M. Coffin, G. J. D'Angio

Hematology/Oncology

Research output: Contribution to journal › Article › peer-review

25 Scopus citations

Abstract

We report an unusual case of peripheral primitive neuroectodermal tumor (pPNET) in an infant presenting with congenital cutaneous nodules and a t(7;22)(p21 ;q11.2). The biologic behavior of the tumor diverged over time from a slowly growing tumor with multiple cutaneous nodules to a more aggressive neoplasm characterized by pulmonary metastases and a soft tissue mass showing additional cytogenetic alterations.

Original language	English (US)
Pages (from-to)	357-363
Number of pages	7
Journal	Medical and Pediatric Oncology
Volume	30
Issue number	6
DOIs	https://doi.org/10.1002/(SICI)1096-911X(199806)30:6<357::AID-MPO10>3.0.CO;2-F
State	Published - 1998

Keywords

Cytogenetics
Pediatrics
Peripheral primitive neuroectodermal tumor

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Oncology
Cancer Research

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10.1002/(SICI)1096-911X(199806)30:6<357::AID-MPO10>3.0.CO;2-F

Cite this

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abstract = "We report an unusual case of peripheral primitive neuroectodermal tumor (pPNET) in an infant presenting with congenital cutaneous nodules and a t(7;22)(p21 ;q11.2). The biologic behavior of the tumor diverged over time from a slowly growing tumor with multiple cutaneous nodules to a more aggressive neoplasm characterized by pulmonary metastases and a soft tissue mass showing additional cytogenetic alterations.",

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AU - Smith, L. M.

AU - Adams, R. H.

AU - Brothman, A. R.

AU - Vanderhooft, S. L.

AU - Coffin, C. M.

AU - D'Angio, G. J.

PY - 1998

Y1 - 1998

N2 - We report an unusual case of peripheral primitive neuroectodermal tumor (pPNET) in an infant presenting with congenital cutaneous nodules and a t(7;22)(p21 ;q11.2). The biologic behavior of the tumor diverged over time from a slowly growing tumor with multiple cutaneous nodules to a more aggressive neoplasm characterized by pulmonary metastases and a soft tissue mass showing additional cytogenetic alterations.

AB - We report an unusual case of peripheral primitive neuroectodermal tumor (pPNET) in an infant presenting with congenital cutaneous nodules and a t(7;22)(p21 ;q11.2). The biologic behavior of the tumor diverged over time from a slowly growing tumor with multiple cutaneous nodules to a more aggressive neoplasm characterized by pulmonary metastases and a soft tissue mass showing additional cytogenetic alterations.

KW - Cytogenetics

KW - Pediatrics

KW - Peripheral primitive neuroectodermal tumor

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Peripheral primitive neuroectodermal tumor presenting with diffuse cutaneous involvement and 7;22 translocation

Abstract

Keywords

ASJC Scopus subject areas

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