Management of the Adult Patient With Congenitally Corrected Transposition: Challenges and Uncertainties

Heidi M. Connolly, William R. Miranda, Alexander Egbe, Carole A. Warnes

Research output: Contribution to journalReview article

Abstract

Congenitally corrected transposition (ccTGA) is a rare form of congenital heart disease characterized by atrioventricular and ventriculoarterial discordance. Patients with ccTGA usually have associated congenital cardiovascular conditions; less than 1% have no associated lesions. Generally, ccTGA is identified during infancy or childhood with features of heart failure or cyanosis when there are associated lesions such as ventricular septal defect and/or pulmonic stenosis. Presentation later in life generally occurs when there are either mild or no associated lesions. Presentation during adulthood may be prompted by symptoms or signs of cardiovascular disease or due to abnormal findings on cardiac testing. Management of patients with ccTGA depends on presentation, symptoms, and associated defects. In this review, we will focus on the management of adult patients with ccTGA.

Original languageEnglish (US)
Pages (from-to)61-65
Number of pages5
JournalSeminars in Thoracic and Cardiovascular Surgery: Pediatric Cardiac Surgery Annual
Volume22
DOIs
StatePublished - Jan 1 2019

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Uncertainty
Cyanosis
Pulmonary Valve Stenosis
Ventricular Heart Septal Defects
Signs and Symptoms
Heart Diseases
Cardiovascular Diseases
Heart Failure

Keywords

  • Congenitally corrected transposition of the great arteries management in adult

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health
  • Surgery
  • Cardiology and Cardiovascular Medicine

Cite this

Management of the Adult Patient With Congenitally Corrected Transposition : Challenges and Uncertainties. / Connolly, Heidi M.; Miranda, William R.; Egbe, Alexander; Warnes, Carole A.

In: Seminars in Thoracic and Cardiovascular Surgery: Pediatric Cardiac Surgery Annual, Vol. 22, 01.01.2019, p. 61-65.

Research output: Contribution to journalReview article

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