Importance of absent ductus arteriosus in Tetralogy of Fallot with absent pulmonary valve syndrome

Muhammad Yasir Qureshi, Harold M. Burkhart, Paul Julsrud, Frank Cetta

Research output: Contribution to journalArticle

7 Scopus citations

Abstract

Tetralogy of Fallot without pulmonary valve syndrome is almost always associated with an absent ductus arteriosus. Patients with right aortic arch and retroesophageal left subclavian artery have a vascular ring if the left ductus arteriosus or its remnant and the Kommerell diverticulum are present. We report the cases of 2 infants in whom the role of an absent ductus arteriosus or its remnant is noteworthy. Both patients had a combination of tetralogy of Fallot with absent pulmonary valve syndrome and right aortic arch with retroesophageal left subclavian artery without a vascular ring. The absence of the ductus arteriosus has a role in the pathogenesis of tetralogy of Fallot with absent pulmonary valve syndrome. The absence of a ductus arteriosus in the right aortic arch with retroesophageal left subclavian artery precludes a vascular ring.

Original languageEnglish (US)
Pages (from-to)664-667
Number of pages4
JournalTexas Heart Institute Journal
Volume41
Issue number6
DOIs
StatePublished - Dec 1 2014

Keywords

  • Aorta/abnormalities
  • Congenital/complications/ diagnosis/genetics/surgery
  • Ductus arteriosus/ abnormalities
  • Heart defects
  • Infant
  • Pulmonary valve/ abnormalities
  • Respiratory insufficiency/etiology
  • Subclavian artery/abnormalities
  • Tetralogy of Fallot/complications

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

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