Importance of absent ductus arteriosus in Tetralogy of Fallot with absent pulmonary valve syndrome

Muhammad Yasir Qureshi, Harold M. Burkhart, Paul Julsrud, Frank Cetta

Research output: Contribution to journalArticle

4 Citations (Scopus)

Abstract

Tetralogy of Fallot without pulmonary valve syndrome is almost always associated with an absent ductus arteriosus. Patients with right aortic arch and retroesophageal left subclavian artery have a vascular ring if the left ductus arteriosus or its remnant and the Kommerell diverticulum are present. We report the cases of 2 infants in whom the role of an absent ductus arteriosus or its remnant is noteworthy. Both patients had a combination of tetralogy of Fallot with absent pulmonary valve syndrome and right aortic arch with retroesophageal left subclavian artery without a vascular ring. The absence of the ductus arteriosus has a role in the pathogenesis of tetralogy of Fallot with absent pulmonary valve syndrome. The absence of a ductus arteriosus in the right aortic arch with retroesophageal left subclavian artery precludes a vascular ring.

Original languageEnglish (US)
Pages (from-to)664-667
Number of pages4
JournalTexas Heart Institute Journal
Volume41
Issue number6
DOIs
StatePublished - Dec 1 2014

Fingerprint

Ductus Arteriosus
Pulmonary Valve
Tetralogy of Fallot
Subclavian Artery
Blood Vessels
Thoracic Aorta
Aortic Arch Syndromes
Diverticulum
Patient Rights

Keywords

  • Aorta/abnormalities
  • Congenital/complications/ diagnosis/genetics/surgery
  • Ductus arteriosus/ abnormalities
  • Heart defects
  • Infant
  • Pulmonary valve/ abnormalities
  • Respiratory insufficiency/etiology
  • Subclavian artery/abnormalities
  • Tetralogy of Fallot/complications

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

Cite this

Importance of absent ductus arteriosus in Tetralogy of Fallot with absent pulmonary valve syndrome. / Qureshi, Muhammad Yasir; Burkhart, Harold M.; Julsrud, Paul; Cetta, Frank.

In: Texas Heart Institute Journal, Vol. 41, No. 6, 01.12.2014, p. 664-667.

Research output: Contribution to journalArticle

Qureshi, Muhammad Yasir ; Burkhart, Harold M. ; Julsrud, Paul ; Cetta, Frank. / Importance of absent ductus arteriosus in Tetralogy of Fallot with absent pulmonary valve syndrome. In: Texas Heart Institute Journal. 2014 ; Vol. 41, No. 6. pp. 664-667.
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