Cone reconstruction of atypical ebstein anomaly associated with right ventricular apical hypoplasia

Gemma Reddin; Joseph T. Poterucha; Joseph A. Dearani; Carole A. Warnes; Frank Cetta

doi:10.14503/THIJ-15-5011

Cone reconstruction of atypical ebstein anomaly associated with right ventricular apical hypoplasia

Gemma Reddin, Joseph T. Poterucha, Joseph A. Dearani, Carole A. Warnes, Frank Cetta

Cardiovascular Surgery

Research output: Contribution to journal › Article › peer-review

5 Scopus citations

Abstract

Cone reconstruction for tricuspid valve repair has revolutionized the surgical treatment of Ebstein anomaly. We present the case of a 58-year-old woman with atypical Ebstein anomaly and right ventricular apical hypoplasia who was spared from palliative shunt physiology by our use of cone reconstruction. Compared with other techniques, cone reconstruction of the tricuspid valve more closely replicates normal valvular anatomy and function. This surgical procedure can be applied to many anatomic variations of Ebstein anomaly, as in our patient’s apparently unique instance of atypical Ebstein anomaly with right ventricular apical hypoplasia.

Original language	English (US)
Pages (from-to)	78-80
Number of pages	3
Journal	Texas Heart Institute Journal
Volume	43
Issue number	1
DOIs	https://doi.org/10.14503/THIJ-15-5011
State	Published - Feb 2016

Keywords

Cardiac surgical techniques
Congenital/complications
Ebstein anomaly/surgery
Heart defects
Heart ventricles/abnormalities
Reconstructive surgical procedures
Right
Treatment outcome
Tricuspid valve/abnormalities/physiopathology/surgery
Ventricular dysfunction

ASJC Scopus subject areas

Cardiology and Cardiovascular Medicine

Access to Document

10.14503/THIJ-15-5011

Cite this

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title = "Cone reconstruction of atypical ebstein anomaly associated with right ventricular apical hypoplasia",

abstract = "Cone reconstruction for tricuspid valve repair has revolutionized the surgical treatment of Ebstein anomaly. We present the case of a 58-year-old woman with atypical Ebstein anomaly and right ventricular apical hypoplasia who was spared from palliative shunt physiology by our use of cone reconstruction. Compared with other techniques, cone reconstruction of the tricuspid valve more closely replicates normal valvular anatomy and function. This surgical procedure can be applied to many anatomic variations of Ebstein anomaly, as in our patient{\textquoteright}s apparently unique instance of atypical Ebstein anomaly with right ventricular apical hypoplasia.",

keywords = "Cardiac surgical techniques, Congenital/complications, Ebstein anomaly/surgery, Heart defects, Heart ventricles/abnormalities, Reconstructive surgical procedures, Right, Treatment outcome, Tricuspid valve/abnormalities/physiopathology/surgery, Ventricular dysfunction",

author = "Gemma Reddin and Poterucha, {Joseph T.} and Dearani, {Joseph A.} and Warnes, {Carole A.} and Frank Cetta",

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doi = "10.14503/THIJ-15-5011",

language = "English (US)",

volume = "43",

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AU - Reddin, Gemma

AU - Poterucha, Joseph T.

AU - Dearani, Joseph A.

AU - Warnes, Carole A.

AU - Cetta, Frank

PY - 2016/2

Y1 - 2016/2

N2 - Cone reconstruction for tricuspid valve repair has revolutionized the surgical treatment of Ebstein anomaly. We present the case of a 58-year-old woman with atypical Ebstein anomaly and right ventricular apical hypoplasia who was spared from palliative shunt physiology by our use of cone reconstruction. Compared with other techniques, cone reconstruction of the tricuspid valve more closely replicates normal valvular anatomy and function. This surgical procedure can be applied to many anatomic variations of Ebstein anomaly, as in our patient’s apparently unique instance of atypical Ebstein anomaly with right ventricular apical hypoplasia.

AB - Cone reconstruction for tricuspid valve repair has revolutionized the surgical treatment of Ebstein anomaly. We present the case of a 58-year-old woman with atypical Ebstein anomaly and right ventricular apical hypoplasia who was spared from palliative shunt physiology by our use of cone reconstruction. Compared with other techniques, cone reconstruction of the tricuspid valve more closely replicates normal valvular anatomy and function. This surgical procedure can be applied to many anatomic variations of Ebstein anomaly, as in our patient’s apparently unique instance of atypical Ebstein anomaly with right ventricular apical hypoplasia.

KW - Cardiac surgical techniques

KW - Congenital/complications

KW - Ebstein anomaly/surgery

KW - Heart defects

KW - Heart ventricles/abnormalities

KW - Reconstructive surgical procedures

KW - Right

KW - Treatment outcome

KW - Tricuspid valve/abnormalities/physiopathology/surgery

KW - Ventricular dysfunction

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Cone reconstruction of atypical ebstein anomaly associated with right ventricular apical hypoplasia

Abstract

Keywords

ASJC Scopus subject areas

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