Cone reconstruction of atypical ebstein anomaly associated with right ventricular apical hypoplasia

Gemma Reddin, Joseph T. Poterucha, Joseph A. Dearani, Carole A. Warnes, Frank Cetta

Research output: Contribution to journalArticle

4 Citations (Scopus)

Abstract

Cone reconstruction for tricuspid valve repair has revolutionized the surgical treatment of Ebstein anomaly. We present the case of a 58-year-old woman with atypical Ebstein anomaly and right ventricular apical hypoplasia who was spared from palliative shunt physiology by our use of cone reconstruction. Compared with other techniques, cone reconstruction of the tricuspid valve more closely replicates normal valvular anatomy and function. This surgical procedure can be applied to many anatomic variations of Ebstein anomaly, as in our patient’s apparently unique instance of atypical Ebstein anomaly with right ventricular apical hypoplasia.

Original languageEnglish (US)
Pages (from-to)78-80
Number of pages3
JournalTexas Heart Institute Journal
Volume43
Issue number1
DOIs
StatePublished - Feb 1 2016

Fingerprint

Ebstein Anomaly
Tricuspid Valve
Anatomic Variation
Anatomy
Right ventricle hypoplasia

Keywords

  • Cardiac surgical techniques
  • Congenital/complications
  • Ebstein anomaly/surgery
  • Heart defects
  • Heart ventricles/abnormalities
  • Reconstructive surgical procedures
  • Right
  • Treatment outcome
  • Tricuspid valve/abnormalities/physiopathology/surgery
  • Ventricular dysfunction

ASJC Scopus subject areas

  • Cardiology and Cardiovascular Medicine

Cite this

Cone reconstruction of atypical ebstein anomaly associated with right ventricular apical hypoplasia. / Reddin, Gemma; Poterucha, Joseph T.; Dearani, Joseph A.; Warnes, Carole A.; Cetta, Frank.

In: Texas Heart Institute Journal, Vol. 43, No. 1, 01.02.2016, p. 78-80.

Research output: Contribution to journalArticle

Reddin, Gemma ; Poterucha, Joseph T. ; Dearani, Joseph A. ; Warnes, Carole A. ; Cetta, Frank. / Cone reconstruction of atypical ebstein anomaly associated with right ventricular apical hypoplasia. In: Texas Heart Institute Journal. 2016 ; Vol. 43, No. 1. pp. 78-80.
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