Unilateral absence of a pulmonary artery (UAPA)

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Abstract

Imaging description Absence or proximal interruption of either the right or left pulmonary artery usually occurs within 1 cm of its origin from the main pulmonary artery [1]. More distal segments of the arteries in the hila are usually present, but are usually diminutive and are supplied by systemic collateral vessels which can arise from bronchial, internal mammary, and intercostal arteries. CT shows the abnormal termination of the pulmonary artery and the collateral vessels supplying the lung (Figure 52.1). Other findings include diminished pulmonary vascularity on that side, decreased size of the affected lung, and a contracted hemithorax. There is also resultant hyperexpansion of the contralateral lung. Left-sided UAPA is often associated with congential anomalies (Figure 52.2), particularly cardiac anomalies such as tetralogy of Fallot and septal defects. Right-sided UAPA is infrequently associated with other congenital anomalies, and is often referred to as isolated UAPA (IUAPA).

Original languageEnglish (US)
Title of host publicationPearls and Pitfalls in Thoracic Imaging
Subtitle of host publicationVariants and Other Difficult Diagnoses
PublisherCambridge University Press
Pages136-137
Number of pages2
Volume9780521119078
ISBN (Electronic)9780511977701
ISBN (Print)9780521119078
DOIs
StatePublished - Jan 1 2011

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ASJC Scopus subject areas

  • Medicine(all)

Cite this

Sykes, A. M. (2011). Unilateral absence of a pulmonary artery (UAPA). In Pearls and Pitfalls in Thoracic Imaging: Variants and Other Difficult Diagnoses (Vol. 9780521119078, pp. 136-137). Cambridge University Press. https://doi.org/10.1017/CBO9780511977701.053