The long QT syndrome.

Research output: Contribution to journalArticle

38 Citations (Scopus)

Abstract

The LQTS is no longer the rare "zebra" whose purpose is to ensure that trainees recall that deafness and sudden cardiac death may be related (Jervell and Lange-Nielsen syndrome). Over the past 10 to 20 years, the number of cases of inherited LQTS (Romano-Ward syndrome) has increased dramatically. It is doubtful that this reflects a true increase in incidence of disease due to a greater rate of sporadic gene mutations occurring in the heart or because of a rising incidence of consanguinity. Rather, the "incidence" of LQTS has risen because of the emerging awareness of and respect for this electrical malady in the heart. Understanding the principal elements of the LQTS, knowing the types of presentations, and being able to identify its presence electrocardiographically will allow the astute physician to expose this silent killer.

Original languageEnglish (US)
Pages (from-to)232-238
Number of pages7
JournalPediatrics in review / American Academy of Pediatrics
Volume19
Issue number7
StatePublished - Jul 1998

Fingerprint

Long QT Syndrome
Jervell-Lange Nielsen Syndrome
Incidence
Romano-Ward Syndrome
Consanguinity
Equidae
Sudden Cardiac Death
Deafness
Physicians
Mutation
Genes

ASJC Scopus subject areas

  • Pediatrics, Perinatology, and Child Health

Cite this

The long QT syndrome. / Ackerman, Michael John.

In: Pediatrics in review / American Academy of Pediatrics, Vol. 19, No. 7, 07.1998, p. 232-238.

Research output: Contribution to journalArticle

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