Severe, Reversible Pulmonary Hypertension in a Patient with Monoclonal Gammopathy and Features of Dermatomyositis

Sheraz Yaqub, Kevin G. Moder, Martha Q. Lacy

Research output: Contribution to journalArticle

15 Scopus citations

Abstract

Pulmonary hypertension is an extremely serious and potentially fatal disorder. Although pulmonary hypertension is a potential complication of connective tissue disease, it has been reported rarely in patients with dermatomyositis. Similarly, multiple myeloma is rare in patients with dermatomyositis. We describe a patient with severe pulmonary hypertension who also had features of dermatomyositis and monoclonal gammopathy. To our knowledge, this is the first reported case of a patient in whom all 3 disorders occurred concurrently. Even more striking is the fact that the patient responded to treatment with cyclophosphamide and prostacyclin. He is asymptomatic more than 5 years after treatment was discontinued.

Original languageEnglish (US)
Pages (from-to)687-689
Number of pages3
JournalMayo Clinic proceedings
Volume79
Issue number5
DOIs
StatePublished - May 2004

ASJC Scopus subject areas

  • Medicine(all)

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