Probable adult polyglucosan body disease

Caroline M. Klein, E. Peter Bosch, Peter J Dyck

Research output: Contribution to journalArticle

10 Citations (Scopus)

Abstract

Adult polyglucosan body disease is a clinicopathologic entity characterized by progressive upper and lower motor neuron dysfunction, sensory loss in the lower extremities, sphincter dysfunction, and occasionally dementia. Pathologically, numerous large polyglucosan bodies are noted in peripheral nerves, cerebral hemispheres, and the spinal cord, as well as in other systemic tissues. We present a case of probable adult polyglucosan body disease based on clinical history and examination, magnetic resonance images, and sural nerve biopsy findings.

Original languageEnglish (US)
Pages (from-to)1327-1331
Number of pages5
JournalMayo Clinic Proceedings
Volume75
Issue number12
StatePublished - 2000

Fingerprint

Sural Nerve
Cerebrum
Motor Neurons
Peripheral Nerves
Dementia
Lower Extremity
Spinal Cord
Magnetic Resonance Spectroscopy
Biopsy
Adult Form Polyglucosan Body Disease
polyglucosan

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Klein, C. M., Peter Bosch, E., & Dyck, P. J. (2000). Probable adult polyglucosan body disease. Mayo Clinic Proceedings, 75(12), 1327-1331.

Probable adult polyglucosan body disease. / Klein, Caroline M.; Peter Bosch, E.; Dyck, Peter J.

In: Mayo Clinic Proceedings, Vol. 75, No. 12, 2000, p. 1327-1331.

Research output: Contribution to journalArticle

Klein, CM, Peter Bosch, E & Dyck, PJ 2000, 'Probable adult polyglucosan body disease', Mayo Clinic Proceedings, vol. 75, no. 12, pp. 1327-1331.
Klein CM, Peter Bosch E, Dyck PJ. Probable adult polyglucosan body disease. Mayo Clinic Proceedings. 2000;75(12):1327-1331.
Klein, Caroline M. ; Peter Bosch, E. ; Dyck, Peter J. / Probable adult polyglucosan body disease. In: Mayo Clinic Proceedings. 2000 ; Vol. 75, No. 12. pp. 1327-1331.
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