Primary melanocytic tumor of the cerebellopontine angle mimicking a vestibular schwannoma: Case report

Mark P. Piedra, Bernd W. Scheithauer, Colin L.W. Driscoll, Michael J. Link

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16 Scopus citations

Abstract

OBJECTIVE: The majority of tumors of the cerebellopontine angle (CPA) are benign. We report the case of a primary malignant melanoma of the CPA that mimicked a vestibular schwannoma (acoustic neuroma). We discuss the differential diagnosis and prognosis of melanotic lesions at this location. CLINICAL PRESENTATION: A 49-year-old man presented with a 7-year history of unilateral deafness and a several month history of imbalance, intractable nausea and vomiting, as well as weight loss. A neurological work-up revealed a large tumor in the left CPA radiographically diagnosed as a vestibular schwannoma. INTERVENTION: A translabyrinthine approach revealed a pigmented, vascular neoplasm encasing vessels and cranial nerves of the left CPA. The tumor was subtotally resected, and a histopathological diagnosis of melanoma was made. The patient had no history of cutaneous melanoma and no other site of disease was ever discovered. CONCLUSION: This case most likely represents primary melanoma of the central nervous system that mimicked a vestibular schwannoma. The differential diagnosis of melanotic lesions of the CPA is discussed as are the prognostic implications of each diagnosis.

Original languageEnglish (US)
Pages (from-to)E206.1-E206.5
JournalNeurosurgery
Volume59
Issue number1
DOIs
StatePublished - Jul 1 2006

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Keywords

  • Acoustic neuroma
  • Melanoma
  • Melanoma mimicking vestibular schwannoma
  • Vestibular schwannoma

ASJC Scopus subject areas

  • Surgery
  • Clinical Neurology

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