Plexogenic pulmonary hypertension associated with POEMS syndrome

Thomas Czeczok, Peter Lin, Eunhee Yi

Research output: Contribution to journalArticlepeer-review

2 Scopus citations

Abstract

Pulmonary hypertension is one of the well-known clinical manifestations of polyneuropathy, organomegaly, endocrinopathy, monoclonal gammopathy, and skin changes (POEMS) syndrome, occurring in approximately 25–30% of the affected individuals. However, the histopathologic spectrum of pulmonary hypertension associated with POEMS syndrome has not been fully documented in the literature. Herein, we report an autopsy case of POEMS syndrome in a patient whose lung tissues showed histopathology indistinguishable from that of idiopathic pulmonary arterial hypertension with abundant plexiform lesions in the small pulmonary arteries.

Original languageEnglish (US)
Pages (from-to)168-170
Number of pages3
JournalRespiratory Medicine Case Reports
Volume22
DOIs
StatePublished - 2017

Keywords

  • POEMS
  • Plexiform
  • Pulmonary hypertension

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine

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