Persistent hypoglycemia in a child with a gastrocolic fistula-an unexpected presentation of leucine-sensitive hypoglycemia

David D. Lee, Edward F. Hollinger, Anthony W. Kim, Mark J. Holterman

Research output: Contribution to journalArticle

Abstract

Leucine-hypersensitive hypoglycemia is a rare clinical entity that is usually diagnosed after an exhaustive search for other causes of hypoglycemia. In nonsurgical patients, an imbalance between metabolic demands and gluconeogenesis are most frequently responsible for recurrent symptomatic hypoglycemia. In the postoperative patient, hypoglycemia more commonly results from inadequate energy intake or malabsorption from functional or anatomical abnormalities. Presented here is an unusual case of a child who was initially diagnosed with postoperative gastrocolic fistula and dumping syndrome as the cause of hypoglycemia but later found to have leucine-hypersensitive hypoglycemia.

Original languageEnglish (US)
JournalJournal of Pediatric Surgery
Volume44
Issue number4
DOIs
StatePublished - Apr 2009
Externally publishedYes

Fingerprint

Hypoglycemia
Leucine
Fistula
Dumping Syndrome
Gluconeogenesis
Energy Intake

Keywords

  • Gastrocolic fistula
  • Hypoglycemia
  • Leucine

ASJC Scopus subject areas

  • Surgery
  • Pediatrics, Perinatology, and Child Health

Cite this

Persistent hypoglycemia in a child with a gastrocolic fistula-an unexpected presentation of leucine-sensitive hypoglycemia. / Lee, David D.; Hollinger, Edward F.; Kim, Anthony W.; Holterman, Mark J.

In: Journal of Pediatric Surgery, Vol. 44, No. 4, 04.2009.

Research output: Contribution to journalArticle

Lee, David D. ; Hollinger, Edward F. ; Kim, Anthony W. ; Holterman, Mark J. / Persistent hypoglycemia in a child with a gastrocolic fistula-an unexpected presentation of leucine-sensitive hypoglycemia. In: Journal of Pediatric Surgery. 2009 ; Vol. 44, No. 4.
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