Outcome of septal myectomy in patients with Fabry's disease

Meghana R. Kunkala, Marie Christine Aubry, Steve R. Ommen, Bernard J. Gersh, Hartzell V. Schaff

Research output: Contribution to journalArticle

4 Scopus citations

Abstract

Fabry's disease has cardiac manifestations that may mimic hypertrophic cardiomyopathy, including left ventricular outflow tract (LVOT) obstruction. It is important to distinguish hypertrophic cardiomyopathy from Fabry's disease, which can be treated with enzyme replacement therapy (ERT). However, after adequate ERT, some patients have no resolution of cardiac symptoms; thus, septal myectomy might be considered. We present 2 cases of extended septal myectomy in patients with LVOT obstruction secondary to Fabry's disease.

Original languageEnglish (US)
Pages (from-to)335-337
Number of pages3
JournalAnnals of Thoracic Surgery
Volume95
Issue number1
DOIs
StatePublished - Jan 1 2013

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ASJC Scopus subject areas

  • Surgery
  • Pulmonary and Respiratory Medicine
  • Cardiology and Cardiovascular Medicine

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