Muscle restricted vasculitis causing dropped head syndrome: A case report and review of the literature

Amy Almaraz Nielsen, Benn E. Smith, Andrew G. Engel, Erich Peter Bosch

Research output: Contribution to journalReview article

1 Scopus citations

Abstract

A 52-year-old man presented with a severe head drop and proximal extremity weakness. Magnetic resonance imaging of the cervical spine showed T2 hyperintensity in cervical paraspinal muscles. Electrodiagnostic studies revealed an axial myopathy isolated to paraspinal muscles. A splenius capitis muscle biopsy confirmed an acute myopathy associated with nonsystemic vasculitis. The patient improved on steroids, intravenous immunoglobulin, and monthly pulse doses of cyclophosphamide. Our case emphasizes that a subgroup of patients with dropped head syndrome have treatable conditions.

Original languageEnglish (US)
Pages (from-to)117-121
Number of pages5
JournalJournal of clinical neuromuscular disease
Volume13
Issue number3
DOIs
StatePublished - Mar 1 2012

Keywords

  • dropped head syndrome
  • electromyography
  • muscle biopsy
  • muscle vasculitis
  • nonsystemic vasculitis

ASJC Scopus subject areas

  • Neurology
  • Clinical Neurology

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