Abstract
Isolated polycystic liver disease (PCLD) is an autosomal dominant disease with genetic and clinical heterogeneity. Apart from liver cysts, it exhibits few extrahepatic manifestations, and the majority of patients with this condition are asymptomatic or subclinical. However, a small fraction of these patients develop acute liver cyst-related complications and/or massive cystic liver enlargement, causing morbidity and mortality. Currently, the management for symptomatic PCLD is centered on palliating symptoms and treating complications.
Original language | English (US) |
---|---|
Pages (from-to) | 181-189 |
Number of pages | 9 |
Journal | Advances in Chronic Kidney Disease |
Volume | 17 |
Issue number | 2 |
DOIs | |
State | Published - Mar 2010 |
Keywords
- Interventions for symptomatic cystic liver disease
- Isolated polycystic liver disease
- Liver cyst-related complications
ASJC Scopus subject areas
- Nephrology