Isolated Polycystic Liver Disease

Research output: Contribution to journalReview article

28 Citations (Scopus)

Abstract

Isolated polycystic liver disease (PCLD) is an autosomal dominant disease with genetic and clinical heterogeneity. Apart from liver cysts, it exhibits few extrahepatic manifestations, and the majority of patients with this condition are asymptomatic or subclinical. However, a small fraction of these patients develop acute liver cyst-related complications and/or massive cystic liver enlargement, causing morbidity and mortality. Currently, the management for symptomatic PCLD is centered on palliating symptoms and treating complications.

Original languageEnglish (US)
Pages (from-to)181-189
Number of pages9
JournalAdvances in Chronic Kidney Disease
Volume17
Issue number2
DOIs
StatePublished - Mar 1 2010

Fingerprint

Cysts
Liver
Asymptomatic Diseases
Genetic Heterogeneity
Morbidity
Mortality
Polycystic liver disease

Keywords

  • Interventions for symptomatic cystic liver disease
  • Isolated polycystic liver disease
  • Liver cyst-related complications

ASJC Scopus subject areas

  • Nephrology

Cite this

Isolated Polycystic Liver Disease. / Qian, Qi.

In: Advances in Chronic Kidney Disease, Vol. 17, No. 2, 01.03.2010, p. 181-189.

Research output: Contribution to journalReview article

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