Intermediate follow-up and predicted survival after the modified Fontan procedure for tricuspid atresia and double-inlet ventricle

R. A. Humes, C. B J Porter, D. D. Mair, M. J. Rice, K. P. Offord, F. J. Puga, Hartzell V Schaff, G. K. Danielson

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Abstract

We reviewed the records of 135 patients with tricuspid atresia and 120 patients with double-inlet ventricle who underwent modified Fontan procedure from 1973 to June 1985. This represents 67% of the total number of patients undergoing the procedure during this period. There were 32 (12%) in-hospital deaths (14 tricuspid atresia, 18 double-inlet ventricle) and 23 late deaths (13 tricuspid atresia, 10 double-inlet ventricle). For patients surviving to hospital dismissal, the 5 year survival was 87%. Follow-up data (mean 3.9 years) were obtained for 157 patients who survived at least 1 year after operation. At last follow-up, of the 157 patients, 92% were in NYHA class I or II, 92% claimed to be improved clinically by the operation, and 98% could work or attend school. Fifty percent were not taking medication at last follow-up. Some degree of edema or ascites was found in 16%. The study showed that (1) the modified Fontan procedure can be performed with low in-hospital mortality (12%) in patients with tricuspid atresia and double-inlet ventricle, (2) hospital survivors have an estimated 5 year survival of 87%, (3) subjectively, functional status is good for hospital survivors at intermediate follow-up, and (4) fluid retention continues to be a problem in a minority (16%) of patients.

Original languageEnglish (US)
Pages (from-to)67-71
Number of pages5
JournalCirculation
Volume76
Issue number3 II SUPPl.
StatePublished - 1987

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Tricuspid Atresia
Fontan Procedure
Survival
Survivors
Hospital Mortality
Ascites
Edema

ASJC Scopus subject areas

  • Physiology
  • Cardiology and Cardiovascular Medicine

Cite this

Humes, R. A., Porter, C. B. J., Mair, D. D., Rice, M. J., Offord, K. P., Puga, F. J., ... Danielson, G. K. (1987). Intermediate follow-up and predicted survival after the modified Fontan procedure for tricuspid atresia and double-inlet ventricle. Circulation, 76(3 II SUPPl.), 67-71.

Intermediate follow-up and predicted survival after the modified Fontan procedure for tricuspid atresia and double-inlet ventricle. / Humes, R. A.; Porter, C. B J; Mair, D. D.; Rice, M. J.; Offord, K. P.; Puga, F. J.; Schaff, Hartzell V; Danielson, G. K.

In: Circulation, Vol. 76, No. 3 II SUPPl., 1987, p. 67-71.

Research output: Contribution to journalArticle

Humes, RA, Porter, CBJ, Mair, DD, Rice, MJ, Offord, KP, Puga, FJ, Schaff, HV & Danielson, GK 1987, 'Intermediate follow-up and predicted survival after the modified Fontan procedure for tricuspid atresia and double-inlet ventricle', Circulation, vol. 76, no. 3 II SUPPl., pp. 67-71.
Humes RA, Porter CBJ, Mair DD, Rice MJ, Offord KP, Puga FJ et al. Intermediate follow-up and predicted survival after the modified Fontan procedure for tricuspid atresia and double-inlet ventricle. Circulation. 1987;76(3 II SUPPl.):67-71.
Humes, R. A. ; Porter, C. B J ; Mair, D. D. ; Rice, M. J. ; Offord, K. P. ; Puga, F. J. ; Schaff, Hartzell V ; Danielson, G. K. / Intermediate follow-up and predicted survival after the modified Fontan procedure for tricuspid atresia and double-inlet ventricle. In: Circulation. 1987 ; Vol. 76, No. 3 II SUPPl. pp. 67-71.
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