IgG4-related systemic disease presenting with lung entrapment and constrictive pericarditis

Hiroshi Sekiguchi, Ryohei Horie, James P. Utz, Jay H. Ryu

Research output: Contribution to journalArticlepeer-review

38 Scopus citations

Abstract

We describe a 29-year-old woman who presented with chronic pleuropericarditis complicated by lung entrapment and constrictive pericarditis. Pleural biopsy performed during the decortication procedure revealed fibrinous pleuritis with lymphoplasmacytic inflammation including IgG4-positive plasma cells. The patient responded favorably to corticosteroid therapy with resolution of pleural effusion and constrictive physiology. To our knowledge, this is the first reported case of IgG4-related systemic disease manifesting as lung entrapment and constrictive pericarditis.

Original languageEnglish (US)
Pages (from-to)781-783
Number of pages3
JournalChest
Volume142
Issue number3
DOIs
StatePublished - Sep 2012

ASJC Scopus subject areas

  • Pulmonary and Respiratory Medicine
  • Critical Care and Intensive Care Medicine
  • Cardiology and Cardiovascular Medicine

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