Extrarenal Wilms' tumor: Results of the National Wilms' Tumor Study

Paul E. Andrews, Panayotis P. Kelalis, Gerald M. Haase

Research output: Contribution to journalArticle

56 Scopus citations

Abstract

Extrarenal Wilms' tumor is extremely rare and occurs predominantly in children. Eight cases of extrarenal Wilms' tumor were reported to the National Wilms' Tumor Study from 1980 to 1986. Patients were followed in the study and not randomized to a particular treatment protocol. Seven patients had a favorable histology. One tumor located in the sacrococcygeal region showed immature teratoma with nephroblastic tissue. The embryogenesis of extrarenal Wilms' tumor is controversial; however, tumor containing teratomatous elements most likely represents a different embryologic origin and, therefore, should be classified separately. All eight patients were treated with operative excision and chemotherapy. Seven of the eight patients were disease-free with a mean follow-up of 34.3 months. It can be inferred from this small group of patients that the prognosis is comparable to intrarenal Wilms' tumor in the National Wilms' Tumor Study.

Original languageEnglish (US)
Pages (from-to)1181-1184
Number of pages4
JournalJournal of pediatric surgery
Volume27
Issue number9
DOIs
StatePublished - Sep 1992

Keywords

  • Wilms' tumor
  • extrarenal

ASJC Scopus subject areas

  • Surgery
  • Pediatrics, Perinatology, and Child Health

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