Abstract
Extrarenal Wilms' tumor is extremely rare and occurs predominantly in children. Eight cases of extrarenal Wilms' tumor were reported to the National Wilms' Tumor Study from 1980 to 1986. Patients were followed in the study and not randomized to a particular treatment protocol. Seven patients had a favorable histology. One tumor located in the sacrococcygeal region showed immature teratoma with nephroblastic tissue. The embryogenesis of extrarenal Wilms' tumor is controversial; however, tumor containing teratomatous elements most likely represents a different embryologic origin and, therefore, should be classified separately. All eight patients were treated with operative excision and chemotherapy. Seven of the eight patients were disease-free with a mean follow-up of 34.3 months. It can be inferred from this small group of patients that the prognosis is comparable to intrarenal Wilms' tumor in the National Wilms' Tumor Study.
| Original language | English (US) |
|---|---|
| Pages (from-to) | 1181-1184 |
| Number of pages | 4 |
| Journal | Journal of Pediatric Surgery |
| Volume | 27 |
| Issue number | 9 |
| DOIs | |
| State | Published - 1992 |
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Keywords
- extrarenal
- Wilms' tumor
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health
- Surgery
Cite this
Extrarenal Wilms' tumor : Results of the National Wilms' Tumor Study. / Andrews, Paul E.; Kelalis, Panayotis P.; Haase, Gerald M.
In: Journal of Pediatric Surgery, Vol. 27, No. 9, 1992, p. 1181-1184.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Extrarenal Wilms' tumor
T2 - Results of the National Wilms' Tumor Study
AU - Andrews, Paul E.
AU - Kelalis, Panayotis P.
AU - Haase, Gerald M.
PY - 1992
Y1 - 1992
N2 - Extrarenal Wilms' tumor is extremely rare and occurs predominantly in children. Eight cases of extrarenal Wilms' tumor were reported to the National Wilms' Tumor Study from 1980 to 1986. Patients were followed in the study and not randomized to a particular treatment protocol. Seven patients had a favorable histology. One tumor located in the sacrococcygeal region showed immature teratoma with nephroblastic tissue. The embryogenesis of extrarenal Wilms' tumor is controversial; however, tumor containing teratomatous elements most likely represents a different embryologic origin and, therefore, should be classified separately. All eight patients were treated with operative excision and chemotherapy. Seven of the eight patients were disease-free with a mean follow-up of 34.3 months. It can be inferred from this small group of patients that the prognosis is comparable to intrarenal Wilms' tumor in the National Wilms' Tumor Study.
AB - Extrarenal Wilms' tumor is extremely rare and occurs predominantly in children. Eight cases of extrarenal Wilms' tumor were reported to the National Wilms' Tumor Study from 1980 to 1986. Patients were followed in the study and not randomized to a particular treatment protocol. Seven patients had a favorable histology. One tumor located in the sacrococcygeal region showed immature teratoma with nephroblastic tissue. The embryogenesis of extrarenal Wilms' tumor is controversial; however, tumor containing teratomatous elements most likely represents a different embryologic origin and, therefore, should be classified separately. All eight patients were treated with operative excision and chemotherapy. Seven of the eight patients were disease-free with a mean follow-up of 34.3 months. It can be inferred from this small group of patients that the prognosis is comparable to intrarenal Wilms' tumor in the National Wilms' Tumor Study.
KW - extrarenal
KW - Wilms' tumor
UR - http://www.scopus.com/inward/record.url?scp=0026657195&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=0026657195&partnerID=8YFLogxK
U2 - 10.1016/0022-3468(92)90782-3
DO - 10.1016/0022-3468(92)90782-3
M3 - Article
C2 - 1331392
AN - SCOPUS:0026657195
VL - 27
SP - 1181
EP - 1184
JO - Journal of Pediatric Surgery
JF - Journal of Pediatric Surgery
SN - 0022-3468
IS - 9
ER -