Ebsteins malformation presenting with tricuspid stenosis: 1-year follow-up after surgical repair

Rami N. Khouzam; Joseph A. Dearani; Paul R. Julsrud

doi:10.1017/S104795111000003X

Ebsteins malformation presenting with tricuspid stenosis: 1-year follow-up after surgical repair

Rami N. Khouzam, Joseph A. Dearani, Paul R. Julsrud

Cardiovascular Surgery

Research output: Contribution to journal › Article › peer-review

Abstract

This is a case of a young woman previously completely healthy, with two uneventful pregnancies and deliveries, who presented with bloating, shortness of breath, and signs of right heart failure. A thorough clinical evaluation, along with a work-up including an echocardiogram and a magnetic resonance imaging revealed the diagnosis of Ebsteins anomaly malformation with tricuspid stenosis. A right ventricular outflow tract obstruction due to thrombus formation was thought to exacerbate her symptoms and lead to the diagnosis. Surgery in the form of right ventricular thrombectomy, right atrial reduction, porcine tricuspid valve replacement and bidirectional cavopulmonary anastomosis bidirectional Glenn, was successfully performed. The patient has been stable clinically more than one year after surgery. Discussion about this rare condition and operative details are provided.

Original language	English (US)
Pages (from-to)	80-85
Number of pages	6
Journal	Cardiology in the young
Volume	20
Issue number	1
DOIs	https://doi.org/10.1017/S104795111000003X
State	Published - Feb 2010

Keywords

Congenital cardiac disease
Ebsteins malformation
Right ventricular outflow tract obstruction
Thrombus

ASJC Scopus subject areas

Pediatrics, Perinatology, and Child Health
Cardiology and Cardiovascular Medicine

Access to Document

10.1017/S104795111000003X

Cite this

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abstract = "This is a case of a young woman previously completely healthy, with two uneventful pregnancies and deliveries, who presented with bloating, shortness of breath, and signs of right heart failure. A thorough clinical evaluation, along with a work-up including an echocardiogram and a magnetic resonance imaging revealed the diagnosis of Ebsteins anomaly malformation with tricuspid stenosis. A right ventricular outflow tract obstruction due to thrombus formation was thought to exacerbate her symptoms and lead to the diagnosis. Surgery in the form of right ventricular thrombectomy, right atrial reduction, porcine tricuspid valve replacement and bidirectional cavopulmonary anastomosis bidirectional Glenn, was successfully performed. The patient has been stable clinically more than one year after surgery. Discussion about this rare condition and operative details are provided.",

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AU - Dearani, Joseph A.

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Ebsteins malformation presenting with tricuspid stenosis: 1-year follow-up after surgical repair

Abstract

Keywords

ASJC Scopus subject areas

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