Ebstein malformation of the tricuspid valve in children, adolescents and young adults

Joseph A. Dearani, Jose Pedro Da Silva, Luciana Fonseca Da Silva, Sameh M. Said

Research output: Chapter in Book/Report/Conference proceedingChapter

Abstract

Ebstein malformation occurs in nearly 1/200,000 live births and accounts for 1 % of all congenital heart diseases. A right ventricular myopathy with varying degrees of failure of tricuspid valve delamination is present in all cases. Consequently, tricuspid valve morphology is highly variable and complex. These unique anatomic features have resulted in an enormous number of different repair techniques. Early results of the “cone repair” are encouragin and this repair represents the most anatomic of all repair techniques.

Original languageEnglish (US)
Title of host publicationPediatric and Congenital Cardiology, Cardiac Surgery and Intensive Care
PublisherSpringer-Verlag London Ltd
Pages1729-1749
Number of pages21
ISBN (Electronic)9781447146193
ISBN (Print)9781447146186
DOIs
StatePublished - Jan 1 2014

Keywords

  • Cone repair
  • Ebstein anomaly
  • Ebstein malformation
  • GOSE score
  • Tricuspid valve repair

ASJC Scopus subject areas

  • Medicine(all)

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