Ebstein Anomaly of the Tricuspid Valve

David J. Driscoll, Joseph A. Dearani

Research output: Chapter in Book/Report/Conference proceedingChapter

1 Citation (Scopus)

Abstract

Ebstein anomaly is rare and presents a spectrum of anatomic and functional severity. Anatomic severity depends on the degree of displacement of the anterior and posterior leaflets of the tricuspid valve into the right ventricle and the size of the resultant right ventricular chamber. Tricuspid regurgitation results. Functional severity is affected by the degree of regurgitation, magnitude of atrial right-to-left shunt, degree of right atrial and ventricular sizes, and ventricular function. Pre-excitation coexists in some patients. Neonates can present in severe distress and with intense cyanosis; they are a therapeutic challenge and have a high mortality. Indications for operation in older patients include cardiac size, ventricular function, and symptoms. A number of techniques have been described to repair the valve and at the time of the operation the atrial communication is also closed.

Original languageEnglish (US)
Title of host publicationPediatric Cardiovascular Medicine
Subtitle of host publicationSecond Edition
PublisherWiley-Blackwell
Pages509-517
Number of pages9
ISBN (Print)9781444335897
DOIs
StatePublished - Jan 13 2012

Fingerprint

Ebstein Anomaly
Tricuspid Valve
Ventricular Function
Tricuspid Valve Insufficiency
Cyanosis
Heart Ventricles
Communication
Newborn Infant
Mortality
Therapeutics

Keywords

  • Ebstein anomaly
  • Pre-excitation
  • Surgery
  • Tricuspid regurgitation
  • Tricuspid valve

ASJC Scopus subject areas

  • Medicine(all)

Cite this

Driscoll, D. J., & Dearani, J. A. (2012). Ebstein Anomaly of the Tricuspid Valve. In Pediatric Cardiovascular Medicine: Second Edition (pp. 509-517). Wiley-Blackwell. https://doi.org/10.1002/9781444398786.ch36

Ebstein Anomaly of the Tricuspid Valve. / Driscoll, David J.; Dearani, Joseph A.

Pediatric Cardiovascular Medicine: Second Edition. Wiley-Blackwell, 2012. p. 509-517.

Research output: Chapter in Book/Report/Conference proceedingChapter

Driscoll, DJ & Dearani, JA 2012, Ebstein Anomaly of the Tricuspid Valve. in Pediatric Cardiovascular Medicine: Second Edition. Wiley-Blackwell, pp. 509-517. https://doi.org/10.1002/9781444398786.ch36
Driscoll DJ, Dearani JA. Ebstein Anomaly of the Tricuspid Valve. In Pediatric Cardiovascular Medicine: Second Edition. Wiley-Blackwell. 2012. p. 509-517 https://doi.org/10.1002/9781444398786.ch36
Driscoll, David J. ; Dearani, Joseph A. / Ebstein Anomaly of the Tricuspid Valve. Pediatric Cardiovascular Medicine: Second Edition. Wiley-Blackwell, 2012. pp. 509-517
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