Descending aortic replacement after Nuss for pectus excavatum in a Marfan patient - Case report

Dawn Jaroszewski, Mennatallah Ewais, Patrick Devaleria, Michael Gotway, D. Craig Miller

Research output: Contribution to journalArticle

Abstract

Introduction The Nuss procedure for pectus excavatum (PE) repair has been successfully performed in Marfan syndrome (MFS) patients however there is concern for future risk of aortic dilation/rupture and need for emergent access with support bars in place. Case presentation We present a 45 year-old male with MFS that required descending aortic replacement shortly after modified Nuss repair. Discussion The majority of MFS patients have severe PE and repair with the Nuss procedure is not uncommon. The risk for life threatening aortic dilation, dissection, or rupture in such patients is a concern when utilizing this technique. Our work has been reported in line with the CARE criteria. Conclusion Nuss repair should be considered in MFS patients with technique modifications and careful consideration of future risk of aortic dilation and rupture.

Original languageEnglish (US)
Pages (from-to)16-19
Number of pages4
JournalInternational Journal of Surgery Case Reports
Volume21
DOIs
StatePublished - 2016

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Funnel Chest
Marfan Syndrome
Dilatation
Aortic Rupture
Dissection
Rupture

Keywords

  • Descending aorta
  • Marfan syndrome
  • Pectus excavatum

ASJC Scopus subject areas

  • Surgery

Cite this

Descending aortic replacement after Nuss for pectus excavatum in a Marfan patient - Case report. / Jaroszewski, Dawn; Ewais, Mennatallah; Devaleria, Patrick; Gotway, Michael; Craig Miller, D.

In: International Journal of Surgery Case Reports, Vol. 21, 2016, p. 16-19.

Research output: Contribution to journalArticle

Jaroszewski, Dawn ; Ewais, Mennatallah ; Devaleria, Patrick ; Gotway, Michael ; Craig Miller, D. / Descending aortic replacement after Nuss for pectus excavatum in a Marfan patient - Case report. In: International Journal of Surgery Case Reports. 2016 ; Vol. 21. pp. 16-19.
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