Cutaneous Polyarteritis Nodosa

Research output: Chapter in Book/Report/Conference proceedingChapter

Abstract

Cutaneous involvement of medium vessel vasculitis most commonly presents with features of inflammatory subcutaneous nodules, purpura, livedo reticularis, and ulceration. The clinical and histopathologic features of isolated cutaneous polyarteritis nodosa (c-PAN) are indistinguishable from the cutaneous involvement of systemic polyarteritis nodosa; however, these conditions differ in their prognosis and treatment. An approach to distinguish between these clinical entities is herein described. In addition, conditions commonly mimicking cutaneous polyarteritis nodosa are reviewed.

Original languageEnglish (US)
Title of host publicationRare Diseases of the Immune System
PublisherSpringer Nature
Pages147-160
Number of pages14
DOIs
StatePublished - 2021

Publication series

NameRare Diseases of the Immune System
ISSN (Print)2282-6505
ISSN (Electronic)2283-6403

Keywords

  • Cutaneous
  • Livedo reticularis
  • Polyarteritis nodosa

ASJC Scopus subject areas

  • Immunology and Allergy
  • Rheumatology
  • Genetics(clinical)

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