Autonomie failure and proximal skeletal myopathy in a patient with primary sjögren syndrome

Paul Sorajja, Maria K. Poirier, John B. Bundrick, Eric L. Matteson

Research output: Contribution to journalArticle

27 Scopus citations

Abstract

Autonomie failure and proximal skeletal myopathy are rare features of the Sjögren syndrome (SS). We describe a 51-year-old woman with primary SS who had development of esophageal dysmotility, urinary retention, severe orthostatism, and skeletal myopathy during a 3-month period after the diagnosis of SS. Her symptoms and signs responded well to corticosteroid therapy. Although dysfunction of the peripheral nervous system has a prevalence rate of 20% in patients with SS, most commonly the nerve dysfunction is a sensory deficit, and autonomie neuropathy is less frequent. Autonomie neuropathy due to SS may be underreported. The cause of our patient's myopathy remains undetermined. We speculate that the myopathy was due to either a form of polymyositis or an immunemediated neuropathy with muscle involvement.

Original languageEnglish (US)
Pages (from-to)695-697
Number of pages3
JournalMayo Clinic proceedings
Volume74
Issue number7
DOIs
StatePublished - Jan 1 1999

ASJC Scopus subject areas

  • Medicine(all)

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