Abstract
Background: The increased incidence of preoperative and postoperative arrhythmia in Ebstein anomaly (EA) prompted some clinicians to perform an electrophysiology study (EPS) in all patients prior to surgery for EA. The cone repair (CR) is the current surgical option of choice for most young patients with EA but the effect of the CR on arrhythmia is not well established. Objectives: To assess the burden of arrhythmia in young patients after CR and to assess the utility of selective preoperative EPS. Materials and Methods: A retrospective review of all patients <21 years of age with EA who had a CR at Mayo Clinic from June 2007 to December 2015 was performed. Surveys were mailed and telephone calls were made to all individuals to assess antiarrhythmic medication use and EP/device procedures performed after CR. Results: There were 143 patients; median age, 10 years (0.1–20.9 years). Thirty-five (24%) patients had a preoperative EPS of which 26 (18%) had a preoperative ablation. Indications for EPS were Wolff–Parkinson–White (WPW), documented arrhythmia, or suspected arrhythmia. Posthospital discharge data were available for 140 (98%) patients. Mean follow-up was 2.9 years (0.1–9.2 years). At follow-up, 7 (5%) patients were receiving antiarrhythmic medications. After CR, only 3 (2%) patients who did not have a preoperative EPS have required an ablation. Conclusions: The risk of arrhythmia after CR for EA in young patients is very low when a preoperative EPS is limited to those with WPW, known arrhythmia, or suspected arrhythmia. In smaller patients, it may be reasonable to defer the EPS.
| Original language | English (US) |
|---|---|
| Pages (from-to) | 26-30 |
| Number of pages | 5 |
| Journal | Congenital Heart Disease |
| Volume | 13 |
| Issue number | 1 |
| DOIs | |
| State | Published - Jan 1 2018 |
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Keywords
- ablation
- arrhythmia
- cone repair
- Ebstein anomaly
- electrophysiology study
- pediatric
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health
- Surgery
- Radiology Nuclear Medicine and imaging
- Cardiology and Cardiovascular Medicine
Cite this
Arrhythmia after cone repair for Ebstein anomaly : The Mayo Clinic experience in 143 young patients. / Wackel, Philip; Cannon, Bryan; Dearani, Joseph; Sessions, Kristen; Holst, Kimberly; Johnson, Jonathan; Cetta, Frank.
In: Congenital Heart Disease, Vol. 13, No. 1, 01.01.2018, p. 26-30.Research output: Contribution to journal › Article
}
TY - JOUR
T1 - Arrhythmia after cone repair for Ebstein anomaly
T2 - The Mayo Clinic experience in 143 young patients
AU - Wackel, Philip
AU - Cannon, Bryan
AU - Dearani, Joseph
AU - Sessions, Kristen
AU - Holst, Kimberly
AU - Johnson, Jonathan
AU - Cetta, Frank
PY - 2018/1/1
Y1 - 2018/1/1
N2 - Background: The increased incidence of preoperative and postoperative arrhythmia in Ebstein anomaly (EA) prompted some clinicians to perform an electrophysiology study (EPS) in all patients prior to surgery for EA. The cone repair (CR) is the current surgical option of choice for most young patients with EA but the effect of the CR on arrhythmia is not well established. Objectives: To assess the burden of arrhythmia in young patients after CR and to assess the utility of selective preoperative EPS. Materials and Methods: A retrospective review of all patients <21 years of age with EA who had a CR at Mayo Clinic from June 2007 to December 2015 was performed. Surveys were mailed and telephone calls were made to all individuals to assess antiarrhythmic medication use and EP/device procedures performed after CR. Results: There were 143 patients; median age, 10 years (0.1–20.9 years). Thirty-five (24%) patients had a preoperative EPS of which 26 (18%) had a preoperative ablation. Indications for EPS were Wolff–Parkinson–White (WPW), documented arrhythmia, or suspected arrhythmia. Posthospital discharge data were available for 140 (98%) patients. Mean follow-up was 2.9 years (0.1–9.2 years). At follow-up, 7 (5%) patients were receiving antiarrhythmic medications. After CR, only 3 (2%) patients who did not have a preoperative EPS have required an ablation. Conclusions: The risk of arrhythmia after CR for EA in young patients is very low when a preoperative EPS is limited to those with WPW, known arrhythmia, or suspected arrhythmia. In smaller patients, it may be reasonable to defer the EPS.
AB - Background: The increased incidence of preoperative and postoperative arrhythmia in Ebstein anomaly (EA) prompted some clinicians to perform an electrophysiology study (EPS) in all patients prior to surgery for EA. The cone repair (CR) is the current surgical option of choice for most young patients with EA but the effect of the CR on arrhythmia is not well established. Objectives: To assess the burden of arrhythmia in young patients after CR and to assess the utility of selective preoperative EPS. Materials and Methods: A retrospective review of all patients <21 years of age with EA who had a CR at Mayo Clinic from June 2007 to December 2015 was performed. Surveys were mailed and telephone calls were made to all individuals to assess antiarrhythmic medication use and EP/device procedures performed after CR. Results: There were 143 patients; median age, 10 years (0.1–20.9 years). Thirty-five (24%) patients had a preoperative EPS of which 26 (18%) had a preoperative ablation. Indications for EPS were Wolff–Parkinson–White (WPW), documented arrhythmia, or suspected arrhythmia. Posthospital discharge data were available for 140 (98%) patients. Mean follow-up was 2.9 years (0.1–9.2 years). At follow-up, 7 (5%) patients were receiving antiarrhythmic medications. After CR, only 3 (2%) patients who did not have a preoperative EPS have required an ablation. Conclusions: The risk of arrhythmia after CR for EA in young patients is very low when a preoperative EPS is limited to those with WPW, known arrhythmia, or suspected arrhythmia. In smaller patients, it may be reasonable to defer the EPS.
KW - ablation
KW - arrhythmia
KW - cone repair
KW - Ebstein anomaly
KW - electrophysiology study
KW - pediatric
UR - http://www.scopus.com/inward/record.url?scp=85041287494&partnerID=8YFLogxK
UR - http://www.scopus.com/inward/citedby.url?scp=85041287494&partnerID=8YFLogxK
U2 - 10.1111/chd.12566
DO - 10.1111/chd.12566
M3 - Article
VL - 13
SP - 26
EP - 30
JO - Congenital Heart Disease
JF - Congenital Heart Disease
SN - 1747-079X
IS - 1
ER -