Anomalies of the fingers and toes associated with Klippel-Trenaunay syndrome

B. J. McGrory, Peter C Amadio, J. H. Dobyns, G. B. Stickler, K. K. Unni

Research output: Contribution to journalArticle

38 Citations (Scopus)

Abstract

Klippel-Trenaunay syndrome is a rare congenital malformation characterized by a large angiomatous nevus; hypertrophy of soft tissue or overgrowth of bone, or both; and venous varicosities. The cases of 108 patients who had a diagnosis of this syndrome between 1956 and 1990 were reviewed. One hundred and twenty-six anomalies were found in twenty-nine patients, each of whom had one to thirteen malformations of the fingers or toes, or both. The ratio of female patients to male patients was approximately two to one. Twenty-six patients had macrodactyly affecting one to six digits; nine, syndactyly involving two or more digits; five, metatarsus primus varus; two, clinodactyly; two, polydactyly; one, camptodactyly; and one, a congenital trigger finger. Thirty-three of the 126 anomalies were in extremities that had no nevi, varicose veins, or generalized hypertrophy.

Original languageEnglish (US)
Pages (from-to)1537-1546
Number of pages10
JournalJournal of Bone and Joint Surgery - Series A
Volume73
Issue number10
StatePublished - 1991

Fingerprint

Klippel-Trenaunay-Weber Syndrome
Toes
Fingers
Nevus
Hypertrophy
Hallux Varus
Syndactyly
Polydactyly
Varicose Veins
Extremities
Bone and Bones

ASJC Scopus subject areas

  • Orthopedics and Sports Medicine
  • Surgery

Cite this

McGrory, B. J., Amadio, P. C., Dobyns, J. H., Stickler, G. B., & Unni, K. K. (1991). Anomalies of the fingers and toes associated with Klippel-Trenaunay syndrome. Journal of Bone and Joint Surgery - Series A, 73(10), 1537-1546.

Anomalies of the fingers and toes associated with Klippel-Trenaunay syndrome. / McGrory, B. J.; Amadio, Peter C; Dobyns, J. H.; Stickler, G. B.; Unni, K. K.

In: Journal of Bone and Joint Surgery - Series A, Vol. 73, No. 10, 1991, p. 1537-1546.

Research output: Contribution to journalArticle

McGrory, BJ, Amadio, PC, Dobyns, JH, Stickler, GB & Unni, KK 1991, 'Anomalies of the fingers and toes associated with Klippel-Trenaunay syndrome', Journal of Bone and Joint Surgery - Series A, vol. 73, no. 10, pp. 1537-1546.
McGrory, B. J. ; Amadio, Peter C ; Dobyns, J. H. ; Stickler, G. B. ; Unni, K. K. / Anomalies of the fingers and toes associated with Klippel-Trenaunay syndrome. In: Journal of Bone and Joint Surgery - Series A. 1991 ; Vol. 73, No. 10. pp. 1537-1546.
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