Congenital intrahepatic arterioportal fistula is a rare entity that most often presents with symptoms of portal hypertension and malabsorption. We discuss a patient who presented with distributive shock, congestive heart failure, pulmonary hypertension, ascites, and a history of severe constipation.
- Congenital fistula
- Down syndrome
- Intrahepatic arterioportal fistula
- Portal hypertension
- Vascular malformation
ASJC Scopus subject areas
- Pediatrics, Perinatology, and Child Health