An unusual presentation of a congenital intrahepatic arterioportal fistula in an infant with Down syndrome

James N. Bogert, D. Dean Potter, Sheri Crow, Grace M. Arteaga, Deborah K. Freese

Research output: Contribution to journalArticle

8 Citations (Scopus)

Abstract

Congenital intrahepatic arterioportal fistula is a rare entity that most often presents with symptoms of portal hypertension and malabsorption. We discuss a patient who presented with distributive shock, congestive heart failure, pulmonary hypertension, ascites, and a history of severe constipation.

Original languageEnglish (US)
Pages (from-to)252-255
Number of pages4
JournalJournal of Pediatric Surgery
Volume46
Issue number1
DOIs
StatePublished - Jan 2011

Fingerprint

Portal Hypertension
Constipation
Down Syndrome
Pulmonary Hypertension
Ascites
Fistula
Shock
Heart Failure

Keywords

  • Congenital fistula
  • Down syndrome
  • Intrahepatic arterioportal fistula
  • Portal hypertension
  • Vascular malformation

ASJC Scopus subject areas

  • Surgery
  • Pediatrics, Perinatology, and Child Health

Cite this

An unusual presentation of a congenital intrahepatic arterioportal fistula in an infant with Down syndrome. / Bogert, James N.; Potter, D. Dean; Crow, Sheri; Arteaga, Grace M.; Freese, Deborah K.

In: Journal of Pediatric Surgery, Vol. 46, No. 1, 01.2011, p. 252-255.

Research output: Contribution to journalArticle

Bogert, James N. ; Potter, D. Dean ; Crow, Sheri ; Arteaga, Grace M. ; Freese, Deborah K. / An unusual presentation of a congenital intrahepatic arterioportal fistula in an infant with Down syndrome. In: Journal of Pediatric Surgery. 2011 ; Vol. 46, No. 1. pp. 252-255.
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