Aggregation-prone c9FTD/ALS poly(GA) RAN-translated proteins cause neurotoxicity by inducing ER stress

Yong Jie Zhang, Karen Jansen-West, Ya Fei Xu, Tania F. Gendron, Kevin F. Bieniek, Wen Lang Lin, Hiroki Sasaguri, Thomas Caulfield, Jaime Hubbard, Lillian Daughrity, Jeannie Chew, Veronique V. Belzil, Mercedes Prudencio, Jeannette N. Stankowski, Monica Castanedes-Casey, Ena Whitelaw, Peter E.A. Ash, Michael DeTure, Rosa Rademakers, Kevin B. BoylanDennis W. Dickson, Leonard Petrucelli

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183 Scopus citations

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Medicine & Life Sciences