A cerebellopontine angle craniopharyngioma in a patient with gardner's syndrome

Case report and review of the literature

Michael J. Link, Colin L W Driscoll, Caterina Giannini

Research output: Contribution to journalArticle

Abstract

A 29-year-old man with a history of Gardner's syndrome presented with a 1-year history of diplopia, right-sided hearing loss, right hypalgesia and dysphagia. A MRI scan revealed a large inhomogeneously enhancing, partially cystic lesion in the right cerebellopontine (CP) angle. There was faint calcification on CT and it was angiographically avascular. A right suboccipital craniotomy was performed with gross total resection of the tumor. The tumor appeared to originate from the right foramen of Luschka. The pathology was consistent with craniopharyngioma. This is only the third reported case of a craniopharyngioma of the CP angle. The pathogenesis and management for this rare occurrence is discussed. The genetics relating tumors in Gardner's syndrome and craniopharyngioma is also reviewed.

Original languageEnglish (US)
Pages (from-to)28
Number of pages1
JournalSkull Base
Volume11
Issue numberSUPPL. 1
StatePublished - 2001

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Gardner Syndrome
Cerebellopontine Angle
Craniopharyngioma
Neoplasms
Diplopia
Craniotomy
Deglutition Disorders
Hearing Loss
Magnetic Resonance Imaging
Pathology

ASJC Scopus subject areas

  • Clinical Neurology

Cite this

A cerebellopontine angle craniopharyngioma in a patient with gardner's syndrome : Case report and review of the literature. / Link, Michael J.; Driscoll, Colin L W; Giannini, Caterina.

In: Skull Base, Vol. 11, No. SUPPL. 1, 2001, p. 28.

Research output: Contribution to journalArticle

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